MCCC2 antibody
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935106861
info@markelab.com
name
MCCC2 antibody
category
Primary Antibodies
provider
FineTest
reference
FNab05048
tested applications
ELISA, WB, IHC
Description
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
Documents del producto
Product specifications
| Category | Primary Antibodies |
| Immunogen Target | methylcrotonoyl-Coenzyme A carboxylase 2 (beta) (MCCC2) |
| Host | Rabbit |
| Reactivity | Human, Mouse, Rat |
| Recommended Dilution | WB: 1:500 - 1:2000; IHC: 1:50 - 1:200 |
| Clonality | polyclonal |
| Conjugation | Unconjugated |
| Isotype | IgG |
| Observed MW | 61 kDa |
| Purity | ≥95% as determined by SDS-PAGE |
| Purification | Immunogen affinity purified |
| Size 1 | 100µg |
| Form | liquid |
| Tested Applications | ELISA, WB, IHC |
| Storage | PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.) |
| UniProt ID | Q9HCC0 |
| Gene ID | 64087 |
| Alias | Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial (MCCase subunit beta),3-methylcrotonyl-CoA carboxylase 2,3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit,3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta,MCCC2,MCCB |
| Background | Antibody anti-MCCC2 |
| Status | RUO |
| Note | Mol. Weight 61 kDa |
Descripción
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MCCC2 antibody
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
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